[Senate Hearing 119-415]
[From the U.S. Government Publishing Office]


                                                     S. Hrg. 119-415

                      FROM REGULATOR TO ROADBLOCK:
                          HOW FDA BUREAUCRACY
                           STIFLES INNOVATION
=======================================================================

                                HEARING

                               BEFORE THE

                       SPECIAL COMMITTEE ON AGING

                          UNITED STATES SENATE

                    ONE HUNDRED NINETEENTH CONGRESS


                             SECOND SESSION

                               __________

                             WASHINGTON, DC

                               __________

                           FEBRUARY 26, 2026

                               __________

                           Serial No. 119-25

         Printed for the use of the Special Committee on Aging
         
[GRAPHIC NOT AVAILABLE IN TIFF FORMAT]         

        Available via the World Wide Web: http://www.govinfo.gov
        
                               __________
                               
                 U.S. GOVERNMENT PUBLISHING OFFICE
63-835 PDF              WASHINGTON : 2026
=======================================================================
       
                       SPECIAL COMMITTEE ON AGING

                     RICK SCOTT, Florida, Chairman

DAVE McCORMICK, Pennsylvania         KIRSTEN E. GILLIBRAND, New York
JIM JUSTICE, West Virginia           ELIZABETH WARREN, Massachusetts
TOMMY TUBERVILLE, Alabama            MARK KELLY, Arizona
RON JOHNSON, Wisconsin               RAPHAEL WARNOCK, Georgia
ASHLEY MOODY, Florida                ANDY KIM, New Jersey
JON HUSTED, Ohio                     ANGELA ALSOBROOKS, Maryland
                              ----------                              
                McKinley Lewis, Majority Staff Director
                Claire Descamps, Minority Staff Director
                        
                        
                        C  O  N  T  E  N  T  S

                              ----------                              

                                                                   Page

Opening Statement of Senator Rick Scott, Chairman................     1
Opening Statement of Senator Kirsten E. Gillibrand, Ranking 
  Member.........................................................     2

                           PANEL OF WITNESSES

Annie Kennedy, Chief Mission Officer, Everylife Foundation for 
  Rare Diseases, Washington, D.C.................................     4
Jeremy Schmahmann, MD, Director, Massachusetts General Hospital 
  Ataxia Center, Boston, Massachusetts...........................     6
Bradley Campbell, President and CEO, Amicus Therapeutics, 
  Princeton, New Jersey..........................................     8
Cara O'Neill, MD, FAAP, Chief Science Officer, Co-Founder, Cure 
  Sanfilippo Foundation, Columbia, South Carolina................    10

                                APPENDIX
                      Prepared Witness Statements

Annie Kennedy, Chief Mission Officer, Everylife Foundation for 
  Rare Diseases, Washington, D.C.................................    34
Jeremy Schmahmann, MD, Director, Massachusetts General Hospital 
  Ataxia Center, Boston, Massachusetts...........................    41
Bradley Campbell, President and CEO, Amicus Therapeutics, 
  Princeton, New Jersey..........................................    45
Cara O'Neill, MD, FAAP, Chief Science Officer, Co-Founder, Cure 
  Sanfilippo Foundation, Columbia, South Carolina................    51

                        Questions for the Record

Annie Kennedy, Chief Mission Officer, Everylife Foundation for 
  Rare Diseases, Washington, D.C.................................    93
Bradley Campbell, President and CEO, Amicus Therapeutics, 
  Princeton, New Jersey..........................................    96

                       Statements for the Record

ALS Association Statement........................................   101
Huntington's Disease Society of America Statement................   103
Jeremy D. Schmahmann, M.D., Statement............................   115
Little Hercules Foundation Statement.............................   165
Individuals with Rare Diseases' Statements for the Record........   169
Taxpayer Protection Alliance Statement...........................   452

 
                      FROM REGULATOR TO ROADBLOCK:
                          HOW FDA BUREAUCRACY
                           STIFLES INNOVATION

                              ----------                              


                      Thursday, February 26, 2026

                                        U.S. Senate
                                 Special Committee on Aging
                                                    Washington, DC.
    The Committee met, pursuant to notice, at 9:35 a.m., Room 
216, Hart Senate Office Building, Hon. Rick Scott, Chairman of 
the Committee, presiding.
    Present: Senator Scott, McCormick, Johnson, Moody, 
Gillibrand, Kim, and Alsobrooks.

                 OPENING STATEMENT OF SENATOR 
                      RICK SCOTT, CHAIRMAN

    The Chairman. Good morning. The U.S. Special Committee on 
Aging will now come to order. Today we are here to ask a simple 
but important question, is the FDA doing everything Congress 
intended it to do to quickly get safe, effective treatments to 
patients with rare diseases who cannot afford to wait?
    For more than 30 million Americans living with a rare 
disease, making sacrifices every day is just a part of life, 
but something they cannot afford to give up is time. Time means 
the ability to walk. Time means independence. Time means being 
able to speak, eat, or even recognize a loved one, and too 
often, time is exactly what patients lose while therapy sit in 
regulatory limbo. Growing up, I saw firsthand how a rare 
disease can affect a family. My family didn't have health 
insurance, and my brother had a rare hip disease. My mom had to 
drive 200 miles round trip just so he could get the care he 
needed. She made that sacrifice because care couldn't wait.
    My brother couldn't afford to sacrifice time. Congress has 
been clear. On an overwhelmingly bipartisan basis we have given 
the FDA flexibility to move faster for patients with serious 
and life-threatening conditions.
    In 2016, Congress passed the 21st Century Cures Act. In 
that bill and other bills that followed, Congress gave 
direction to the FDA, encouraged the use of real-world 
evidence, highlighting that rare disease drug development 
requires adaptability and urgency.
    These laws are meant to help cut through bureaucratic 
delays and give patients access to the care and cures they so 
desperately need. Yet here we are, 10 years later, hearing from 
patients, physicians, and drug developers that the system is 
not working as Congress intended.
    I have heard from Commissioner Makary that he is working 
hard to fix longstanding problems at the FDA and I want to 
thank him for the work he is doing to try and make a strained 
system work better for patients. However, advocates here today 
will describe inconsistent review practices, shifting 
standards, and redundant, often late appearing data requests 
that in many cases may not be driven by safety concerns but by 
an overly cautious and rigid approach that puts bureaucratic 
processes ahead of patients.
    As we will hear, the human cost of this regulatory slow 
walking is real. Many of the patients affected by these delays 
have no other treatment options. Patients from every State come 
and talk to our offices, and I am sure the same thing with the 
Ranking Member, sharing their irreversible declines in health 
that happen while they or someone they care about waits for a 
treatment that might never come.
    It is heartbreaking to hear from families who are left 
watching their loved ones deteriorate, while promising 
therapies remain stuck in review. Meanwhile, small biotech 
companies struggle to survive years of uncertainty, even when 
their science is sound. Beyond individual patients, there are 
serious national security consequences that come with the FDA's 
inaction and delays.
    Our adversaries have been accelerating their drug 
development and approval, attracting investment, talent, and 
clinical trials. FDA inaction here at home creates an economic 
and national competitive issue. Let me be clear, this hearing 
is not about weakening safety standards. Safety must always 
come first, but safety and speed are not mutually exclusive.
    A system can protect patients while still acting with 
urgency, transparency, and common sense. Some of you may be 
asking why the Senate Aging Committee is tackling this issue 
when so many of those impacted by issues with rare disease 
treatments are young. Here is why. Part of caring for America's 
aging population is making sure that more Americans are given 
the opportunity to grow old.
    It may sound cliche, but we are all aging. If something is 
standing in the way of a younger American making it to their 
senior years, it is absolutely the business of this Committee 
and something we need to try and fix. It is my hope that 
today's hearing will serve as a useful tool to help us 
understand what we can do to bring accountability, 
transparency, and efficiency to the process.
    We are joined by an incredible panel of witnesses here 
today representing a wide range of perspectives, but all 
working toward a better future for people living with rare 
diseases. Now, we have a lot of members in the crowd that are 
here because rare disease drugs are very important to them, and 
I want to thank everybody for being here. Now, I would like to 
recognize Ranking Member Gillibrand for her opening statement.

                 OPENING STATEMENT OF SENATOR 
             KIRSTEN E. GILLIBRAND, RANKING MEMBER

    Senator Gillibrand. Thank you, Chairman Scott. I really 
appreciate you calling today's hearing. Thank you to our 
witnesses and the advocates who are here for Rare Disease Day 
on the Hill. It makes a big difference that you come together 
to make sure your loved ones are being heard and that the 
challenges and struggles that you go through as families and 
supporters are being understood by lawmakers.
    Every one of us in this room today knows that when we have 
a friend, or a loved one, or a family member who has a rare 
disease, that the most important thing is finding a cure, 
getting the treatment, and making sure they survive. A disease 
is considered rare if it affects fewer than 200,000 people, but 
rare diseases actually aren't that rare. One in ten Americans 
is living with a rare disease.
    As you know, many of these patients face substantial unmet 
medical needs. Because it can be really difficult and expensive 
for companies to develop these treatments and the FDA to 
evaluate them, Congress has provided the agency with 
significant regulatory flexibility to encourage both biotech 
innovation and rare disease therapies.
    These include authorizing the accelerated approval pathway 
to speed up the drug review, establishing programs like the 
Rare Disease Endpoint Advancement Pilot to bolster novel 
endpoint development, and strengthening and expanding the use 
of patient experience data and real-world evidence in drug 
reviews.
    These mechanisms are designed to help improve access to 
novel treatments for our patients, and they are supposed to 
provide drug sponsors with a predictable and consistent 
approach to addressing regulatory science challenges that are 
unique in rare disease therapy development and review, like 
designing complex clinical trials, developing appropriate 
endpoints, and using real world evidence, but it is not working 
how it should be. FDA's approach, transparency, and flexibility 
varies widely between its offices, divisions, and centers. I 
have seen a pattern of hesitation to use authorized 
flexibilities, limited communication with drug sponsors, 
failure to incorporate patient experience in real world 
evidence reviews, and FDA shifting its regulatory position on 
trial design at the last minute, rejecting drug applications, 
and requiring new clinical trials the sponsor may be unable to 
perform. This is heartbreaking for patients, and it is why we 
can't afford delays and disruptions in treatment.
    Rare diseases can progress rapidly, cause irreversible 
harm, and in some cases premature death. This is also 
frustrating for drug sponsors who face increased costs and 
delayed timelines that impact the viability of their clinical 
trials, particularly in the United States. Uncertainty shapes 
behavior across the biotech ecosystem.
    Without consistency and predictability, drug sponsors will 
continue to struggle with seeking FDA approval and will take 
their clinical trials elsewhere, like to China. This is bad for 
business, and it is bad for patients. If we want the U.S. to 
remain the global leader in biotech and we want American 
patients to have access to these novel treatments, things need 
to change.
    Congress must hold the FDA accountable. We must make sure 
FDA fixes its inconsistent and unpredictable application of 
regulatory flexibility. It is essential for supporting 
innovation, while upholding the highest standard for safety and 
efficacy, in the approval of these rare disease drugs.
    FDA appears to be moving in the right direction. With the 
rare disease evidence principles, the rare disease innovation 
hub, proposing new pathways for approval and trying to hire 
more reviewers, but it doesn't matter what agency leadership 
puts in a press release. It is about execution and 
implementation across all levels of that agency. Consistency 
from top to bottom.
    Congress will ensure that happens by conducting oversight, 
encouraging application of authorized flexibilities, and 
providing adequate resources to restore agency capacity. I look 
forward to hearing from our witnesses and working with this 
committee to hold the FDA accountable because rare disease 
patients cannot wait.
    The Chairman. Thank you, Ranking Member. I would like to 
welcome our witnesses, experts who are here to talk about how 
serious this issue is and the steps we can take to ensure 
patients with rare diseases are not left behind by regulatory 
delay. First, I want to recognize Annie Kennedy, Chief Mission 
Officer at the EveryLife Foundation for Rare Diseases.
    Ms. Kennedy is a nationally recognized leader in rare 
disease policy and patient advocacy and works directly with 
patients, caregivers, and families navigating the drug 
development and approval process.
    EveryLife represents the voices of rare disease communities 
across the country, and has long advocated for patients 
centered policies, regulatory flexibility, and timely access to 
life-saving therapies. Thank you for being here, and please 
begin your testimony.

           STATEMENT OF ANNIE KENNEDY, CHIEF MISSION

               OFFICER, EVERYLIFE FOUNDATION FOR

                RARE DISEASES, WASHINGTON, D.C.

    Ms. Kennedy. Thank you, Chairman Scott, Ranking Member 
Gillibrand, and distinguished members of the Committee for 
convening this critical hearing. I am Annie Kennedy, Chief 
Mission Officer for the EveryLife Foundation for Rare Diseases. 
I am honored to be here alongside the hundreds of advocates who 
have joined us for Rare Disease Week on Capitol Hill.
    Collectively, we are representing the more than 30 million 
Americans living with rare diseases. Today, there are more than 
10,000 known rare diseases, about 70 percent of which start in 
childhood. For small patient communities facing progressive 
diseases, time is a commodity.
    Traditional large placebo-controlled trials are often 
neither feasible nor ethical when considering the challenges 
and urgency of rare diseases. Beginning with the passage of the 
Orphan Drug Act in 1983, your leadership has provided tools 
that have rocketed the U.S. into the most competitive developer 
of rare disease products. Each landmark law since has reshaped 
our landscape.
    In fact, tomorrow marks an anniversary of another watershed 
moment for our community here on Capitol Hill. The MD Care Act 
hearing convened in this exact same hearing room, presided over 
by Senator Arlen Specter, included a 13-year-old named Benjamin 
Cumbo. Twenty-five years ago, I watched with great pride as Ben 
asked Congress for actions that could help cure him and his 
friends so that he could achieve his dreams of growing up, 
having a girlfriend, and serving his country.
    Congress did respond. In that time, Congress has built a 
framework that incentivizes rare product development, 
authorizes regulatory flexibility, creates new pathways to 
approval, and embeds patient experience into review. While 
fewer than five percent of rare diseases currently have an FDA 
approved treatment, nearly 1,400 orphan-designated therapies 
are now changing the lives of patients and families.
    Recently, this momentum has shifted. We are here today 
because our community has experienced worrisome trends with 
devastating consequences. While we are heartened by recent 
announcements of therapy development initiatives, such as the 
Rare Disease Evidence Principles Framework and the Plausible 
Mechanism Pathway and are eager to work with the agency on 
their implementation, our rare disease community has 
experienced a series of product application actions that seem 
misaligned with these recent public pledges to expand the use 
of regulatory flexibility.
    Since the start of 2025, we have seen at least 23 complete 
response letters declining to approve rare disease therapies, 
many under accelerated approval, that suggest a hesitation to 
apply regulatory flexibility through surrogate endpoints, 
natural history studies, and external controls.
    At that same time, advisory committee meetings for drugs 
and biologics declined by 65 percent compared to 2024, reducing 
opportunities for external expertise and patient insights to 
inform complex rare disease product decisions. We asked 
families who would been personally affected by recent 
regulatory decisions to reflect on their impact. These stories 
will be shared for the record. Story after story spoke to 
chilling consequences of recent regulatory delays and clinical 
trial hurdles.
    As one mom shared about her son, Stone. My son is now 
receiving this experimental treatment, and he is thriving. For 
the first time since his diagnosis, his doctors have told us, 
with this treatment, a near normal lifespan is within reach for 
a disease that once came with a teenage expiration date that is 
nothing short of extraordinary. We are now living in fear, not 
because science failed, not because companies stopped fighting 
rare diseases, but because of regulatory inconsistency.
    We are here today because congressional action is needed to 
ensure that this generation of patients will benefit from our 
existing rare disease treatment pipelines. We ask that Congress 
engage FDA to clarify its approach to accelerated approval for 
rare diseases, its consistent application of regulatory 
flexibility, and to urge the resumption of advisory committee 
meetings so that external expertise informs complex reviews.
    We also urge Congress to resource the Rare Disease 
Innovation Hub to strengthen cross center coordination and to 
establish the Rare Disease and Condition Advisory Committee and 
a science focused drug development initiative. In closing, 25 
years ago, I stood in this room filled with rare families.
    Today, advances in science have put life-altering 
treatments within reach for many, but those advances were not 
in time for those who were in this with me 25 years ago. While 
Ben achieved many of his dreams, he died two days before 
receiving his master's degree. We now have the opportunity to 
ensure that this generation of rare disease patients will 
benefit from today's therapy development pipelines.
    Each time a promising therapy faces delays or demise, 
investment wanes, future scientific promise is unfulfilled, and 
lives are lost. Time is the most precious commodity for our 
rare disease community.
    As Stone's mom implored while writing from his hospital 
bedside, we are closer than ever to rewriting the future of 
these diseases. Please don't let my generation become the next 
group of mothers who stand at gravesides instead of 
graduations. Thank you.
    The Chairman. Thank you. Thank you, Ms. Kennedy. Now, I 
would like to introduce Dr. Jeremy Schmahmann, Professor of 
Neurology at Harvard Medical School, Founding Director of the 
Ataxia Center at Massachusetts General Hospital, and Principal 
Investigator for the Laboratory for Neuroanatomy. I said that 
correct, right?
    He is a leading neurologist who treats patients with 
progressive and neurodegenerative diseases where time and 
access to treatment are critical. He has seen firsthand the 
consequences of delayed access to care and the irreversible 
loss patients can experience while waiting for regulatory 
decisions.
    His testimony will round today's discussion and the real-
world clinical impact these regulatory delays have on patients 
and families. Thank you for being here. Please begin your 
testimony.

         STATEMENT OF JEREMY SCHMAHMANN, MD, DIRECTOR,

             MASSACHUSETTS GENERAL HOSPITAL ATAXIA

                 CENTER, BOSTON, MASSACHUSETTS

    Dr. Schmahmann. Chairman Scott, Ranking Member Gillibrand, 
members of the Committee, thank you for convening this hearing, 
and for the opportunity to testify, and for your remarkable 
opening statements.
    My name is Jeremy Schmahmann. I am the Martha and Robert 
Fogelman Chair in Ataxia, and Cerebellar Neurology at 
Massachusetts General Hospital, and Professor of Neurology at 
Harvard Medical School. I started the first Ataxia Center in 
the country, and I have cared for patients with spinocerebellar 
ataxias for 45 years.
    I am the site principal investigator for Biohaven's study 
of troriluzole in ataxia and my comments today reflect my 
personal and professional opinion, not necessarily that of my 
employer.
    Senators, please help us fix the FDA. It has rejected 
troriluzole, a drug that is safe--the first treatment to 
improve quality of life and slow progression in spinocerebellar 
ataxia. My patient Steve, for example, developed 
spinocerebellar ataxia type 3, also known as Machado-Joseph 
disease, in his late 30's.
    Like his mother before him, he will become increasingly 
disabled, will need to use a wheelchair, become bedridden, and 
die young, but since starting troriluzole a year ago, he has 
not changed. Mary, in her late 40's, has type two. After six 
and a half years on troriluzole, she has not change.
    These inherited neurodegenerative diseases worsen 
inexorably and in this business, staying the same is success. 
Like other rare diseases, ataxia is difficult to study, 
deteriorates slowly, and manifests differently even within 
families. There are 15,000 ataxic patients in America. Some 
affect hundreds of people, some just a few.
    Now, Congress, as you have told us, recognized these 
challenges and passed legislation mandating that FDA use 
regulatory flexibility and real-world evidence in rare diseases 
like ataxia. The drug riluzole, used to treat ALS for 50 years, 
was reported to improve ataxia.
    Based on this, and the plausible mechanism of action in 
spinocerebellar ataxia, Biohaven developed troriluzole, which 
metabolizes into riluzole, but is taken once a day with better 
brain penetration and fewer side effects. Early in the drug's 
development, an ataxic patient who stopped treatment after a 
year of open label therapy insisted they go back on troriluzole 
because they told us their condition worsened after stopping 
the drug.
    Biohaven, to their credit, provided troriluzole to these 
patients and ran a one-year, double-blind placebo-controlled 
study. Patients with spinocerebellar ataxia type three improved 
compared to placebo. They were falling less, and they had fewer 
injuries. Biohaven requested approval of troriluzole for 
spinocerebellar ataxia type three based on these results.
    The FDA refused to review the new drug application. 
Biohaven obtained FDA feedback and used a revised protocol to 
follow patients on drug for another three years, comparing them 
with patients in two natural history studies. In this real-
world evidence study, troriluzole showed significant 
improvement across nine pre-specified FDA endpoints, slowing 
disease by 50 to 70 percent.
    This is a dramatic result that was supported by patient and 
physician feedback. We were all shocked when FDA denied 
approval of this safe drug that makes people better. I wrote 
six letters to FDA leadership between 2023 and 2025, co-signed 
by 17 ataxia colleagues, asking FDA to review the application 
again and work with Biohaven to make the drug available, if 
necessary performing post-marketing studies. I never heard 
back.
    Now, 300 patients, stable on troriluzole, will have to come 
off drug, and they are distraught. I met three times with FDA's 
Center for Drug Evaluation and Research. On each occasion, they 
did not heed the patients or the experts or considered the 
science. One panel member said to me, why should I listen to 
you?
    The FDA's proposed path forward is another placebo-
controlled trial that will take five to eight years, or a 
randomized withdrawal of the drug from patients benefiting from 
it. If this happens, patients on placebo will die. I believe 
this to be unethical, lacking charity, mercy, or kindness.
    Senators, please, save our patients' lives. Use your 
authority to require that FDA consider real-world evidence and 
applies the regulatory flexibility you have legislated, and in 
so doing restore transparency, integrity, and competence to the 
agency. Thank you.
    The Chairman. Now, I would like to recognize Ranking Member 
Gillibrand to introduce our next witnesses.
    Senator Gillibrand. Thank you, Mr. Chairman. I want to 
introduce our next witness, Bradley Campbell. Mr. Campbell is 
the President and CEO of Amicus Therapeutics, a biotechnology 
company focused on discovering and developing new medicines for 
people living with rare diseases.
    During his tenure at Amicus, he led the global 
commercialization of Galafold, a medication used to treat Fabry 
disease in adults, which was approved by the U.S. Food and Drug 
Administration on an accelerated basis. Mr. Campbell brings 
over 20 years of experience in the rare and orphan disease 
fields. You may begin your testimony.

       STATEMENT OF BRADLEY CAMPBELL, PRESIDENT AND CEO, 
           AMICUS THERAPEUTICS, PRINCETON, NEW JERSEY

    Mr. Campbell. Thank you very much, Chairman Scott, Ranking 
Member Gillibrand, the rest of the Senators on the Committee. 
It is my privilege to be here today to speak to you about our 
experience in developing drugs for people living with rare 
diseases. I am also honored to be alongside my fellow 
panelists.
    I feel far less qualified than they to speak today, but I 
hope I can share some perspectives on the challenges and 
opportunities we have to help fix the system. I have had the 
privilege to work at Amicus for the last 20 years and have 
dedicated most of my professional career to developing new 
treatments for people living with rare diseases.
    I thought I could begin with a patient story that I think 
captures the spirit of the testimony here today and the 
conversation we are having. At a recent patient meeting, we 
were discussing patient experience data and how we might make 
endpoints for clinical trials more meaningful for patients.
    During a break, a young woman with Pompe disease took me 
aside and said, what would be most meaningful for her is if she 
could breathe on her own for just one minute. That would make 
the difference between her life and her death. This is not an 
approvable endpoint in Pompe disease, of course, but she 
depends upon a mechanical ventilator to breathe.
    If that ventilator fails, if the battery dies, if an aid 
fails to clear a mucus plug, just that 60 seconds of her own 
breath could make the different between her life and death. I 
think that comment is a very powerful reminder of why patients 
and caregivers must help us design better clinical studies with 
real endpoints that make a difference for them.
    We can't ask patients to wait for years before approved 
treatments come when the difference between life and death can 
be that single breath. I think the rare disease innovation 
ecosystem in the United States has made enormous progress over 
the last 20 years, but it must now again adapt in speed, 
agility, and flexibility to keep the pace of innovation.
    One of our own development experiences at Amicus I think 
sheds light on how regulatory flexibility and working together 
with sponsors and regulators can make a real difference in drug 
development. When we were developing our medicine Galafold for 
Fabry disease, we learned in early studies that in some 
patients the drug worked and some patients it didn't.
    Through careful data analysis and close collaboration with 
the FDA and regulators around the world, we developed an assay 
that could identify which of the thousands of genetic variants 
that cause Fabry disease might best respond to the therapy, and 
just as importantly, which ones may not.
    The FDA ultimately incorporated that assay into our label 
and approved the first ever oral precision medicine for people 
living with Fabry disease. What does that mean? That means when 
sponsors and regulators work together, the result was an oral 
treatment option that has saved thousands of patients' years of 
biweekly infusions.
    We know rare diseases are biologically complex. We know 
they are difficult to study. As we sit here today, 95 percent 
of the more than 10,000 known rare diseases lack an FDA-
approved treatment. I think that is statistic many of us are 
familiar with, but if you fast forward that pace of 
development, it will take us 150 years to only treat half of 
the remaining rare diseases.
    Small and mid-sized biotechnology companies like Amicus, 
Biohaven, and others are the engine of rare disease innovation, 
but they can only succeed if the regulatory system adapts along 
with unmet medical need. I think there are three practical 
areas that we can work together to improve that very system.
    First, we must start clinical trials faster. We know in 
other countries, those trials start in weeks, not months. We 
can reduce administrative requirements, leverage single IRBs, 
use AI and other digital tools to get into the clinic faster. 
We also must find better ways to measure efficacy. We can use 
biomarkers, innovative endpoints, accelerated approvals.
    These are things the FDA has at its disposal right now, but 
we must use them more and we can make manufacturing inspections 
and rules work better. The single biggest delay oftentimes is 
inspections for getting patients access to medicines.
    The FDA has tools like remote interactive inspections and 
relying on global regulators to reduce that inefficiency and 
let me close with just one final story. At a patient meeting 
last year, a man with Fabry disease told us when he was 
diagnosed in his 30's, he stopped saving for retirement because 
he thought there was no reason to think he could live that 
long. Fast forward 15 years, Fabry disease is now a treatable 
disease.
    Advancement in treatments have changed that trajectory and 
for the first time he is thinking about a future he thought he 
would never have. I look forward to working together with the 
members of this Committee, and indeed with the regulators, the 
broad community here focused on rare diseases to find ways to 
ensure that we have a flexible, adaptable, agile regulatory 
system that can keep pace with modern innovation.
    Thanks so much for the opportunity to testify and I look 
forward to taking your questions.
    Senator Gillibrand. Thank you, Mr. Campbell. I want to move 
to introduce our next witness, Dr. Cara O'Neill. Dr. O'Neill is 
the Co-Founder and Chief Science Officer at the Cure 
Sanfilippo--the Cure Sanfilippo Foundation, dedicated to 
accelerating scientific development on disease and empowering 
families with the resources they need to navigate their 
journey.
    Dr. O'Neill founded the foundation after receiving her 
daughter, Eliza, Sanfilippo's diagnosis in 2013. At the 
foundation, Dr. O'Neill leads patient focused research efforts 
and awareness, working to bridge the gap between scientists, 
clinicians, industry, and family.
    She was awarded the International 2020 Patient Advocacy 
Leader Award by World Symposium for exceptional contributions. 
You may begin your testimony.

           STATEMENT OF CARA O'NEILL, MD, FAAP, CHIEF

          SCIENCE OFFICER, CO-FOUNDER, CURE SANFILIPPO

              FOUNDATION, COLUMBIA, SOUTH CAROLINA

    Dr. O'Neill. Thank you, Chairman Scott, Ranking Member 
Gillibrand, and members of the Committee. On behalf of 15 
million children with rare diseases in this country, I thank 
you truly for your concern.
    I am Cara O'Neill, Chief Science Officer at Cure Sanfilippo 
Foundation, a Pediatrician, and mom to Eliza who has an ultra-
rare genetic disease called Sanfilippo Syndrome, or MPS3, one 
of many forms of childhood dementia leading to progressive, 
irreversible brain damage. I would like to first acknowledge 
the critical public service of FDA and its staff who shoulder 
complex and heavy workloads every day.
    We know the pressures are significant because we feel it 
too. Of late, we have seen many press releases highlighting new 
FDA policies and programs, which encourage us to look out into 
the future with hope, but today, the Committee has called us 
here with the recognition that current regulatory barriers are 
significantly impacting patients right now, and never more 
starkly than for degenerative conditions where time is the most 
crucial factor and where every regulatory flexibility must be 
leveraged to meet this uniquely urgent need.
    We can see this illustrated in a story of three girls with 
the same deadly disease, but very different lives. Isabelle, or 
Izzy, was the first child with Sanfilippo that my husband and I 
met after our own daughter Eliza's diagnosis. Izzy was just 11, 
and the disease had already taken a tremendous toll. She could 
no longer walk independently, taking only a few steps if her 
mom held most of her weight.
    Izzy had lost the ability to speak years before and could 
no longer eat or drink without choking, so relied on a feeding 
tube. She had seizures and increasingly severe abnormal 
movements that twisted her arms and legs into painful 
positions.
    During one visit, Izzy's mom shared that she had come to 
accept this disease would take her daughter's life, but what 
she said next has always stuck with me. She said, in truth, I 
fear her suffering more than I fear death. At that time, my 
Eliza was close to four and in an extremely hyperactive stage 
of the disease, but she sang and talked with us. She played 
dress up and clapped around the house in my high heels. She 
rode her tricycle everywhere. She looked so healthy, but what 
was going on inside her body and brain was a much different 
picture.
    Meeting Izzy put us face to face with Eliza's future, the 
concrete and cruel reality of what this disease would do. A 
medicine didn't come in time for Izzy. She suffered greatly and 
passed away just a few weeks before her 15th birthday. For 
decades, we have known the cause of this disease. We can 
precisely measure the levels of toxic biomarker to determine 
whether a treatment is working and now we have the science to 
treat it.
    Thanks to NIH funding and support from nonprofit 
foundations, including our own, a promising gene therapy was 
developed and propelled toward clinical trial at nationwide 
Children's Hospital in Ohio. While we anxiously were awaiting 
news the trial will begin, back at home we watched Eliza's 
sentences becoming shorter, her words less frequent. She became 
agitated and hardly slept.
    The disease was taking hold. Two years later, in May 2016, 
the clinical trial finally began and Eliza, then six and a 
half, was so very lucky to be the first child to receive that 
gene therapy. It was her chance at a life different from 
Izzy's--a chance to grow up. Now at 16, it is clear that 
therapy changed her life. She surpassed average life 
expectancy, runs on the beach, plays in the water, uses picture 
cards to tell us how she is feeling and what show she wants to 
watch on TV. She can feed herself and goes to school every day.
    These are simple but incredibly meaningful abilities that 
have a huge impact on her daily life, and children treated with 
higher doses earlier in life have even more remarkable 
outcomes. Like Caroline, who is now 10. She can read, play on a 
softball team, and learn to ski on her recent family vacation.
    Despite these breakthroughs and nearly 10 years after the 
trial began, families outside the trial are still waiting for 
access. Why? Because last summer the drug was denied approval, 
not because of safety or how the children were benefiting, but 
for questions about manufacturing.
    While this is an important issue, FDA could have used its 
flexibility to continue reviewing the application while 
addressing questions in parallel. You see, early on, trial data 
confirmed the drug's mechanism was more than just plausible, it 
was biologically effective, showing significant reduction of 
toxic biomarker within just six months after treatment in all 
the children.
    Granting accelerated approval based on this biomarker would 
have brought treatment access to children years earlier, 
preventing further brain damage and changing the lives of so 
many children, like Sadie, who is here today--who is still 
waiting. This same drug application was recently resubmitted, 
but FDA issued another denial asking for yet more paperwork 
before agreeing to review it again.
    Congress has given FDA the tools of flexibility it needs to 
accelerate approvals for these devastating diseases, but sadly 
flexibility and speed are not actually what most rare disease 
patients are witnessing.
    Transformative therapies are at FDA's doorstep and so, with 
great respect, families are pleading for FDA to unlock the door 
and move with urgency so that our children can have a chance at 
the life they deserve. Thank you.
    The Chairman. Thank you for your testimony. Thank you, Mr. 
Campbell, for your testimony. Now we will go to questions. 
Senator Johnson.
    Senator Johnson. Thank you, Mr. Chairman. Again, I have to 
commend you for another excellent hearing here. At the start of 
the hearing, I received a text from Laura McLinn, who reminds 
me that 10 years to this day, as Chairman of Homeland Security 
I held a hearing titled, Connecting Patients to New and 
Potential Life Saving Treatments. Her son, Jordan, who suffered 
from Duchenne Muscular Dystrophy testified at hearing--was 
certainly present there.
    Two years later, that resulted in Right to Try, which was 
not easy to pass. I had to hold up the FDA user fee bill, had 
to water down Right to Try quite a bit to make sure that Big 
Pharma wouldn't sabotage it. They did sabotage it over in the 
House, but because of President Trump's leadership, he forced 
the House to pass the Senate version. Its main benefit is its 
name. It is very limited in its application, unfortunately.
    People have the right to try. Laura has also begged me, 
begged me in a text to mention Ataluren and Deramiocel, two 
investigatory drugs that are also being held up by the FDA for 
Duchenne Muscular Dystrophy. I think we probably are going to 
need another piece of legislation, probably Right to Try 2.0--
something that is going to be far more effective than the 
current Right to Try, but I will tell you, reading this 
testimony this morning, you can maybe tell just by my passion, 
it enraged me.
    It enraged me that these families, these patients are being 
denied effective treatments because of the regulatory 
roadblocks. Quick story and again, I want to ask questions, but 
a quick story. After I met the Duchenne Muscular Dystrophy 
community, they went up before a panel of FDA--this was 
probably in 2016, 1917, or 1918--begging. There are about 60 
Duchenne Muscular patients' families begging the FDA, please 
approve this investigatory drug for our children.
    Again, time is muscle, time is brain and that panel, I 
don't know who sat on it, listened to those 60 families begging 
them and said no, just like they said no--and I can't even 
pronounce these diseases and drugs. They say no time and time 
and time again. That has to change. Congress is directing the 
FDA, be more flexible--say yes.
    You know, these patients understand the risks. They ought 
to have the right to try. Dr. Schmahmann--am I pronouncing that 
right?
    Dr. Schmahmann. Yes, sir.
    Senator Johnson. I don't want you throwing anybody under 
the bus because I don't want this to impact future approvals 
but describe your meetings with CDER. To me, it is shocking to 
have one of those members of that panel say, why should we 
listen to you? Well, because you are a doctor at Harvard.
    You are treating patients. You are having success. You are 
giving them a new lease on life, and you have got bureaucrats 
inside these agencies saying, why the hell should we listen to 
you? I want you going into greater detail--describe what those 
meetings are like.
    Dr. Schmahmann. Thank you, Senator. We have heard a few 
words a few times. Heartbreaking as the experience of patients 
and families going through this and the compassion that is 
required.
    I saw none of that in the three meetings with the FDA. The 
members of the panel were like talking to a brick wall. There 
was no engagement, no dialog. In fact, they said as much, this 
is not a dialog, this is not a collaboration. They do not seem 
to see the suffering of the patients, and they didn't hear the 
science.
    They were rigid and inflexible and unyielding. The FDA 
worked with the company initially, but then they changed their 
mind later, and so, as the studies unfolded, everything came to 
a grinding halt. This drug in particular is safe. It 
metabolizes into a drug that has been there for 30 years in the 
market and is safe. Patients say it works. The doctors say it 
works. The study shows it works.
    The double-blind first study showed it worked. The real-
world evidence shows it works. Patients behind me, every one of 
them, talking to them yesterday, say it works. This drug works.
    To paraphrase the Senator, what is their problem? My 
experience of the people on that panel, three times, as a 
private citizen coming for the first time to the FDA, was 
deeply distressing.
    Senator Johnson. I have already texted Dr. Tracy Beth Hoeg 
and told her I have read your testimony. I will be sending her 
your testimony. I hope she listens to this. If I could just 
take a couple more minutes, Dr. O'Neill, you are obviously 
personally impacted by this.
    Can you describe any meetings you have had similar to what 
we just heard? Again, the American people need to understand 
what these regulators are doing and not doing. Dr. O'Neill.
    Dr. O'Neill. Thank you. You know, I will say that my 
interactions with regulators have been kind, so maybe a bit of 
a different perspective is they have listened. They have been 
interested to hear what we had to say. To hear the patient 
perspective. I think where we are challenged is that we don't 
see that translated into regulatory action.
    Some of the decisions that are coming out are not 
benefiting patients right now. Listening is great, but two-way 
conversation and collaboration is actually what is needed, and 
greater transparency in how patient experience data and patient 
input is actually being integrated into these decisions.
    Senator Johnson. My guess is that panel for Duchenne 
Muscular Dystrophy back in 2017 or whatever probably listened 
very nicely to the families, but they still said no. That is an 
unacceptable answer.
    Again, you have my commitment. I am going to delve into 
this. We are going to right these wrongs. Thank you. Mr. 
Chairman, this is again an excellent hearing. We have got to 
followup on this. This is just completely unacceptable. Thank 
you
    The Chairman. Thank you, Senator Johnson. Senator 
Alsobrooks.
    Senator Alsobrooks. Thank you so much, Chair Scott. Also 
Ranking Member Gillibrand. I am so grateful to be here today 
joined by so many patient advocates, caregivers, family 
members.
    I have heard from many Marylanders living with rare 
diseases and from their families, including dozens who have 
visited my office this week to share their priorities and their 
concerns. As I underscored with the NIH Director a few weeks 
ago, patients suffering from devastating diseases do not have 
time to wait for needless delays to critical cures. For 
Marylanders with rare diseases, delayed access is not just an 
inconvenience, it is a matter of life or death.
    For many with rare conditions, clinical trials are their 
last and best hope. These patients also depend on a regulatory 
process that is science driven and capable of turning research 
into real treatment. Instead of strengthening those 
foundations, this Administration is constantly disrupting 
clinical trials, slowing innovation, and undermining the 
pipeline to cures.
    Scientific integrity should always guide decision-making, 
and we must protect the firewall between the Food and Drug 
Administration and political influence. President Trump and 
Secretary Kennedy continue to decimate critical parts of that 
system. The instability they have caused ripples across 
families, physicians, researchers, and innovators, and patients 
pay the price.
    Ms. Kennedy, I would like to ask, over the past two weeks, 
we saw a striking example of political interference at the FDA 
involving a seasonal mRNA flu vaccine from Moderna. The agency 
first declined even to review the application, then reversed 
course just one week later after revised regulatory approach.
    The abrupt change raised serious concerns about 
transparency, predictability, and political influence in what 
should be a scientific process. An episode many have described 
as regulatory whiplash. What does that kind of volatility 
signal about how the FDA is functioning right now, and why does 
that matter for rare disease reviews that depend on regulatory 
consistency?
    Ms. Kennedy. First of all, thank you so much, Senator, for 
being here and for all of you being here today, and for this 
important issue. I think first it is important to say that I am 
not an expert in vaccines, and I am here really to focus on 
rare disease, but I appreciate the question really asking about 
the trends that we are seeing and us being here really trying 
to follow the trends and understand what that means for rare 
disease.
    I also agree with Dr. O'Neill that we have seen real 
intention from career staff and staff scientists at FDA around 
their engagement, but what we are concerned about is, to your 
question, what seems to be reversals in decisions, where there 
had been previous agreement, previous work with sponsors that 
was directing sponsors to move in one direction, and then 
regulatory decisions seemed to be yielding different decisions 
at this point.
    As I stated in my testimony, we have seen recently 23 
complete response letters issued in rare diseases that are 
delaying access to the patient community and having devastating 
consequences to our community. Many of those actually are 
decisions that are reversals in regulatory agreements that have 
been made previously.
    Additionally, we are very concerned that previously, if 
there were to be a complex decision that needed to be worked 
through between a sponsor and the agency, an advisory committee 
would have been convened, and we have seen 65 fewer advisory 
committees convened in 2025 than 2024.
    In fact, none since July. We are very concerned that the 
regulatory tools that are at the disposal of the agency to 
really work through some of these really complex decisions 
aren't being utilized.
    Senator Alsobrooks. Thank you. Just very quickly, if I can 
also go to Ms. O'Neill. Finding new cures doesn't happen 
overnight, and it rarely happens in a single year.
    Breakthrough therapies are built over decades of careful 
scientific work and discoveries, and NIH funded laboratories 
form the foundation for treatments that later move into 
clinical trials through regulatory review and ultimately into 
patient care.
    When NIH research capacity is disrupted, as we have seen, 
and weakened, how does that set back the search for new cures 
long before therapies ever reach the FDA?
    Dr. O'Neill. Thank you for your question. The NIH is a 
critical source of funding for innovation in this country and 
scientific innovation. It is interesting that when there were 
disruptions and uncertainty in the funding, we received a flood 
of requests about funding from our small non-profit foundation. 
I think non-profit foundations across the country were seeing 
that and, you know, we are not equipped to take up all of the 
pre-clinical and transformative science that NIH can do. The 
role of the NIH in supporting innovation is huge.
    Senator Alsobrooks. Thank you.
    The Chairman. Thank you, Senator. Senator McCormick.
    Senator McCormick. Thank you, Mr. Chairman and thanks to 
you and the Ranking Member for convening this and thank you all 
so much for being here today to help bring some of these 
critical issues to Americans and Pennsylvanians to light. Ms. 
Kennedy, more than 30 million Americans live with rare 
diseases, yet fewer than five percent have an approved 
treatment.
    As you mentioned, since early 2025, the FDA has issued at 
least 23 complete response letters for rare disease therapies, 
while advisory committees use has declined dramatically. When 
late-stage rare disease applications raise concerns, what 
alternatives to issuing a complete response letter should the 
FDA use, including advisory committees or structured post-
approval commitments, to resolve issues without restarting the 
entire process?
    Ms. Kennedy. Thank you. We appreciate that question. FDA 
has at its disposal, thanks to Congress, many types of 
engagements between sponsors and the agency. Many of those have 
been made possible thanks to the user fees.
    We are concerned that many of those meetings and meeting 
types aren't occurring, and that the CRLs are being utilized as 
a way to perhaps maybe even clear the docket or create delays. 
There could be a lot of reasons why that might be happening, 
but there are meeting types that have been implemented that 
could enable engagement to answer questions that sponsors, and 
the agency might have.
    We saw actually the agency deploy this during the pandemic, 
the COVID pandemic, where we saw real rapid, real time 
resolution to a crisis in our country and the agency was able 
to interact with sponsors. Get questions answered in real time 
and then we saw that CBER tried to operationalize that in other 
places and spaces.
    We would really, as a rare disease community, like to see 
that operationalized within rare disease because we believe 
that our rare disease community has the urgency and unmet need 
that matches that of a pandemic, of a crisis.
    We have individuals in this room who have very limited life 
expectancies. If we don't address what is happening in rare 
diseases with that same sense of urgency, they would not be 
here with us if we were to convene this hearing another year 
from now.
    Senator McCormick. Thank you. Thank you for highlighting 
that urgency, and I think we feel it, and you are helping us to 
feel it. Thank you for that. Mr. Campbell, just on the issue of 
accelerating the process.
    I was taken by the fact in preparing for this that some 
countries are moving much faster on rare disease therapies. The 
European Union's FAST-EU program caps multinational clinical 
trial authorization at 70 days. Australia allows many trials to 
begin almost immediately after an ethics approval.
    What is going on here? What will happen if the United 
States fails to keep pace? What policy changes should we 
consider in the Congress, given what appears to be a much more 
streamlined approach in other places?
    Mr. Campbell. Thank you, Senator. I completely agree. I 
think, you know, the United States has been the beacon of 
biotechnology innovation for so many decades, and it is part of 
why we have more therapies approved today for rare diseases 
than we did, you now, decades ago.
    I would acknowledge legislation like the Orphan Drug Act 
that led to that. As we said in our testimony and many of the 
panelists here today, we have now stopped keeping pace with 
innovation and I think one exact point, which I raised in my 
testimony as well, is speed to clinical trials. For me, on the 
one hand it is time for patients, and taking weeks, 70 days, 
would be a remarkable number.
    I think Congress could work with the FDA to pass 
legislation to encourage, again, centralized IRBs, leveraging 
digital technology and artificial intelligence to help us do 
that. Reducing regulatory requirements. For sure, those things 
could speed us into the clinic. The other piece, I think, which 
is sitting behind this is our national competitiveness and in 
some ways our national security.
    When we think about Australia, we think of Europe, 
collaborative nations, etcetera--there are other nations out 
there that perhaps we see in a different way, and from my 
perspective, whether you think of that as a security threat or 
whether you think of that as a threat to getting drugs to 
patients, in either case, I think Congress can take a 
leadership role in helping the FDA to speed through that 
process.
    Senator McCormick. Thank you all for being here.
    The Chairman. Thank you, Senator McCormick. Senator Kim.
    Senator Kim. Thank you, Chairman. Thank you to all of you 
coming out here. A couple words I just heard that I think 
really just hit the nail on the head. I would love your 
reactions to it. When we are talking about all the different 
problems that we are facing with the FDA, the bureaucracy or 
the workforce issues, I think the word that really hits it home 
is urgency.
    I heard you use that. You know, I heard use that Ms. 
Kennedy. I feel like that is really what we are talking about 
here. Is like we need a government that is moving at the speed 
of urgency that the parents are trying to save their kids, 
right. Like, that we are struggling to understand what the 
actual purpose here is and the speed with which we need to 
move. Look, I got two boys. I got an eight-year-old and a ten-
year-old. I would do anything for them, you know.
    I just like, how do we translate that into the urgency of a 
government trying to be responsive? I think that is where some 
of the disconnect hits on so many levels. You know, Mr. 
Campbell, you talked about it. You used the word national 
security. I used to work in national security. I was in 
Afghanistan and Iraq and elsewhere.
    I saw this government move with urgency when they felt like 
lives were on the line, but like, why is it that we can't 
necessarily translate that to another circumstance where there 
are millions of lives on the lines and people just don't have 
the time to wait for this? I think that that is really a 
purpose. How do we talk about this as a national security 
priority?
    The same reason we are trying to save lives abroad is the 
same reasons we are trying to save the lives here at home. Does 
that make sense to you, Ms. Kennedy? Am I kind of grasping the 
crux here of what we are trying to push forward?
    Ms. Kennedy. Yes, Senator, you absolutely are. Congress has 
recognized this urgency in statute and has enabled the use of 
regulatory flexibilities, and that is what is reflected in the 
accelerated approval pathway and the use of surrogate outcome 
measures and biomarkers in clinical trial design in rare 
disease.
    What we are concerned about is that in many of these 
complete response letters, what we are seeing reflected is FDA, 
especially in one of the medical product centers, CBER, seems 
to be the trend that we are detecting backing away from a 
comfort level or use of the surrogate biomarkers.
    What we have seen in rare disease is surrogates work. 
Surrogate biomarkers do save lives. We have more than 250 
products that have been approved through the accelerated 
approval pathway, but fewer than 20 percent of those are for 
the non-oncologic, non-infectious rare diseases.
    Which means there is a distinction between what is 
happening in the rare community that is in this room and the 
broader rare community. It is really important when we look at 
those statistics that we sort of look at what the different 
medical product centers are comfortable with and are doing, and 
that is why we--we know that the tools are available. We want 
to ensure that they are being utilized.
    Senator Kim. Mr. Campbell, I wanted to bring you in on this 
because, you know, you have talked about this at length. Build 
off of what we just heard. How would expand use of adaptive 
trial designs or surrogate endpoints by the FDA lend itself to 
achieving better outcomes when it comes to rare disease 
approvals?
    Mr. Campbell. Yes, I think the first step is just use what 
we have available to us, right. If you look at oncology, I 
think in 2024, there were 8,000 different therapeutics in 
clinical trials that dwarfs the number in rare diseases today.
    I think a large part of that is the much more welcoming use 
of accelerated approval and surrogate biomarkers. Our own 
product, Galafold, was approved on a surrogates biomarker. The 
competitor product also, Fabrazyme, was approved on a surrogate 
biomarker and these things work. I get it, you know, rare 
diseases are biologically complex.
    It is very difficult to understand how long it is going to 
take. You can't do randomized control studies in the same way 
you can with broader disease populations. When it is done 
right, as in the case of Fabrazyme, 10 years later, after using 
real-world evidence and a registry, they are able to confirm 
the original surrogate endpoint, and now it is a fully approved 
product. For me, the tools are all there. It is really more, as 
we have discussed, consistency and using the tools that exist. 
If we were to--oh please, go ahead, Senator.
    Senator Kim. I just want to jump in here at the end. I mean 
the urgency on the trials and moving up forward on the 
approvals, but Mr. Campbell, I also want to raise another 
issue, which is just how long it often takes to build 
manufacturing facilities here in the United States.
    You know, the level of slowness with the inspections 
themselves. I want that urgency on a manufacturing side as 
well. You know, what can you be showing us about the 
decisionmakings that manufacturers are going through especially 
in terms of being able to build this and manufacture this here 
in America.
    Mr. Campbell. Here at home. Thank you so much for the 
opportunity to address that, so just by background, Amicus, we 
work with external manufacturers. As a small cap company, we 
don't have the capital to build our own manufacturing 
facilities, and we certainly don't have an environment to be 
able to do that.
    We work outside the United States. It takes three to five 
years to just to build a state-of-the-art manufacturing 
facility for protein therapeutics. It takes another one to two 
years then to get that facility inspected. You are talking five 
to seven years from when we want to do this to when it actually 
has medicine coming off the line for patients. In my mind, it 
is mutually beneficial to all of us, so create incentives--and 
they don't have to be financial incentives. Help with 
permitting. Help with inspections.
    Give priority to inspections for homegrown manufacturing 
facilities. Create an environment that is actually supportive 
of bringing manufacturing at home, versus using, which is what 
we have seen over the last couple of years, more sticks to try 
to prevent--probably a more qualified person to speak to this, 
speaking in background. Let's use incentives instead of sticks 
to encourage that because I think the United States ecosystem, 
the patients, all benefit from doing that.
    Senator Kim. Mr. Chair, you know, we have talked at length 
here in this Committee about the benefits on so many levels of 
having that manufacturing here in America, the speed with which 
we can move, the capabilities.
    You know, these are some very concrete things that I hope 
we can followup on and really come up with a game plan here 
because it is just, honestly, it is just pathetic that we are 
just not able to do this with a greater level of speed given 
the skills and the talent and the resources of our country. We 
can and should be doing better.
    Thank you for holding this hearing today.
    The Chairman. Thank you, Senator Kim. Senator Johnson, do 
you have some more questions?
    Senator Johnson. Yes. Thank you, Mr. Chairman. I mean, I 
think the elephant in the room here is, so we have got the laws 
in place. They maybe could be beefed up, but I think it is a 
personnel issue, right. I fear that not even necessarily the 
heads of the agencies, but possibly bureaucrats that have been 
there for decades, for whatever reason, they don't like a 
particular drug, and so they are able to sabotage it.
    My question, how can we overcome the inconsistency from, 
you know, one bureaucrat to the next bureaucrat, changing 
administrations, or quite honestly, you know, a particular 
bureaucrat that has been in there for decades that just keeps 
blocking things. I mean, how do you get to the personnel issue? 
I will start with you, Ms. Kennedy.
    Ms. Kennedy. I think my experience differs from some on 
this panel in that we have seen great examples of models where 
we have had public meetings and public workshops where FDA has 
come together with the patient community, which I think is an 
incredibly important mechanism, to have meetings where we can 
have regulatory agreement around the use of certain innovative 
models in clinical trial design, surrogate endpoints, natural 
history studies as a control arm that had then allowed those 
programs to move forward.
    Senator Johnson. I pointed out in a meeting like that, a 
panel, for Duchenne Muscular Dystrophy, 50 to 60 families, and 
they still said no.
    Ms. Kennedy. I love that reference. What you may not know, 
you probably don't know, is prior to being with the EveryLife 
Foundation, I was with the Duchenne community, and so that may 
have been an advisory committee.
    Senator Johnson. Were you in that meeting?
    Ms. Kennedy. Yes, I was. Well, it depends on what meeting 
you are referring to. If it was an ADCOM, an advisory committee 
meeting, that advisory committee did vote no, but then the 
agency brought that internally and then overruled that.
    Senator Johnson [continuing]. overruled it.
    Ms. Kennedy. That is a perfect example of the agency still 
has the authority to make the decision because they heard from 
the community and what we are concerned about right now is that 
the agency isn't engaging with the patient community.
    Senator Johnson. Dr. O'Neill, in your testimony you talked 
about, you got your CO, the complete response letter. I mean, 
perfect bureaucratic type of--in other words, the no letter, 
right, and you got the no letter, not necessarily because of 
safety or lack of efficacy. It was because there is something 
in the manufacturing process, which again, a manufacturer, I 
understand that, but can you explain that. It seems like a 
pretty weak excuse where you could, we will fix the 
manufacturing process so this drug can be made available just 
talk about that
    Dr. O'Neill. Thank you. I am not an expert on gene therapy 
manufacturing, so I will say that. However, the sponsor was 
very transparent in reviewing the full CRL with our community 
so that we could understand truly what the concerns were. Many 
of them were noted to be things like a crack on the floor not 
in the manufacturing area, or a tarp that was out back, or 
things that really are unrelated to our children.
    Senator Johnson. Trust me, I have been through audits. I 
supplied packaging material for medical devices. You can find 
an excuse to, you know, write something up, pretty flimsy 
excuses.
    Again, that is my concern. Dr. Schmahmann, in your case, it 
was based on real world evidence. It seems like the real-world 
evidence was completely in favor of allowing patients access to 
this drug. Talk a little bit about, you know, why you got a 
CLR, a no letter.
    Dr. Schmahmann. Thank you, Senator. You know, one of the 
thoughts that came to me as we are going through this whole 
process and hearing what happened to Sanfilippo with the crack 
in the floor in the factory is that this is a policy of death 
by technicality. These little, tiny glitches that the FDA is 
producing land up not approving drugs and patients die as a 
consequence.
    I am glad to hear that there are people in the FDA who are 
doing what Congress requires them to do, but that speaks to the 
unpredictability and the erratic nature of the responses and 
the performance of the people in FDA. There are many ways to go 
forwards to use clinical trials and then use the new technology 
to bring treatments to patients faster that are safe and make a 
difference.
    Science advances. The regulation is keeping up with the new 
advances, but it seems like the FDA is having trouble with 
that. The FDA must keep pace with the updates in science using 
the biomarkers, serum or imaging, using digital markers, using 
patient reported outcomes.
    I developed the patient reported outcome measure for 
ataxia, understanding what patients are saying. The key issue 
here is that the real experts are the patients. The patients 
are the experts by experience. The patients are our research 
collaborators. We are all patients. Every one of us has 
something.
    We are all patients. It may not be a rare disease, but this 
applies to us. We are talking about us, whether it is a rare 
disease or not. The approach that can be taken, including what 
was started at our institution, I think called a platform 
trial, where you can have one small group of controls and a 
number of other patient cohorts trying different drugs. There 
are innovations both in the clinical trial design and the 
biomarker space.
    This is where we need to move, and the urgency is exactly 
what Senator Kim was talking about. There is an urgency now and 
some of the drugs on the table now, the ones you have heard 
about from Dr. O'Neill and myself, these should be approved 
this week. There is no reason not to.
    Going forward, we need to find a way to enhance, to 
expedite, and make this a better process and have a sense that 
when you are going to the FDA, you know what you are getting. 
It is not just a random scatterplot of who is going to get what 
kind of a person there.
    Senator Johnson. Isn't another root cause here is literally 
the doctors are no longer at the top of the treatment pyramid? 
They have been replaced by regulators. You talk patients are 
number one, but doctors are the ones that are most 
knowledgeable in this equation, and you are shutting off to the 
side. What you are saying doesn't count because the regulators 
have replaced you in terms of making these decisions for 
patients. Isn't that a big problem?
    Dr. Schmahmann. You know, Senator, on your wall in your 
office yesterday, I saw your mission statement, which was 
triple, teamwork, respect, integrity, professionalism, loyalty, 
and education.
    The FDA is not doing that. It is the opposite. 
Communication, dialog, teamwork between the physicians, the 
patients, the pharma who make the drug, the regulators, that is 
a two-way street. It is a dialog. In medicine, when we do 
rounds in the morning on our patients in the hospital, there is 
a discussion.
    The physician is there, the residents are there, the nurse, 
the nurse practitioner, or the physical therapist, the patient 
and the family. It is a conversation, a discussion. This is not 
what we are hearing from across the board and certainly from 
the other rare diseases. We are here, the few of us.
    Turns out there are 30 million people behind us, as you 
said. What we are bringing to you is the plea to make the FDA 
what it was supposed to be, which is what you regulated, and 
allow us to work in a collaborative manner across the board, 
not with this kind of hit or miss approach as to who you are 
going to get on a committee. You are looking for 
accountability.
    In fact the leadership of the FDA, it is their 
responsibility to hold the feet to the fire of the people under 
that person's leadership. Not just to say good things, but to 
actually make them happen and bring new drugs to the American 
population including us, our patients, my patients, that are 
safe and effective.
    Senator Johnson. Again, thank you, Mr. Chairman. I think 
this is an excellent hearing, excellent testimony. Both you and 
the ranking member, you pretty well diagnosed the problem here. 
I mean, in your opening statements, you laid out the problems. 
This is eminently fixable, and we have to fix it. Again, I am 
committed to working with you to do so but thank you for this 
hearing.
    The Chairman. Senator Gillibrand.
    Senator Gillibrand. Thank you. In 1972, the Federal 
Advisory Committee Act established advisory committees within 
the FDA to help provide independent expert scientific input on 
product reviews and policy topics.
    In 2025, FDA canceled many advisory committee meetings and 
indicated that it would like to move away from involving 
advisory committees in the review of drug applications. For 
each of the witnesses, you can start Ms. Kennedy, how important 
is it to the rare disease community for FDA to restore the use 
of advisory committees?
    Ms. Kennedy. It is everything. We yesterday had one of our 
communities showcase in front of close to 800 members of the 
rare disease community how an advisory committee meeting helped 
inform a key regulatory decision for the VAR syndrome community 
by showing how an open public hearing enabled members of that 
community illuminate the nuance of a very complex regulatory 
decision in a very complicated regulatory review.
    As Senator Johnson just highlighted, I have been a part of 
many advisory committee meetings for communities, including the 
Duchenne community, and advisory committees don't always vote 
yes. That is not the point.
    The point is for external experts, including clinicians, 
including those with statistical expertise and manufacturing 
expertise that are not always internal to the agency, to be 
brought to bear on regulatory decisions because we realize that 
with 10,000 rare diseases, it is not possible for FDA to always 
have all of that expertise internal.
    Those committee hearings must be at the avail of the 
agency, but also those open public hearings must be available 
so that patient communities who are participating in clinical 
trials can share what their experiences in those clinical 
trials are. One of the challenges we have in clinical trial 
design is we don't always know what we are going to find when a 
clinical trial begins.
    We design a clinical trial hoping that we are going to be 
able to select the best outcome measures, but sometimes patient 
communities who participate in those trials experience other 
benefits and those hearings enable us to hear from patients 
about what other outcomes were achieved so that we can make the 
best decisions possible for the patient community around safety 
and efficacy.
    Eliminating those hearings eliminates the chance for FDA to 
make the decisions that are in the best interests of the 
patient communities possible.
    Senator Gillibrand. Dr. Schmahmann and Dr. O'Neill, 
congressional actions have advanced how patient experience data 
is included in the development and evaluation of rare disease 
therapies. What is the importance of the patient voice in this 
regulatory process, and what more is needed to ensure FDA 
includes this information in its decisionmaking?
    Dr. Schmahmann. I agree that it is critical, Senator. I 
think that there is a deeper problem. If you don't listen to 
somebody else's advice in a complex story, that is the opposite 
of humility. It is a denial of the patient's humanity and it is 
sort of hubris. You don't want to hear what the patients have 
to say? Who are you? That is the problem.
    This is all about the patients. To deny the patient voice 
in drug development and in drug design--and I agree completely 
with Ms. Kennedy here. Determining the end point when you start 
is fine if the disease is well known in the millions of people.
    In our case, for example, the spinocerebellar ataxia, the 
first clinical trials that Biohaven did in the 2016s, we didn't 
know what would change. We had to take a guess and I worked 
with them in devising the scale, devising a trial. The patients 
then told us, you know what, I am falling less, I am not as 
fatigued, and my speech is better. There was a different 
outcome we didn't understand at the beginning. That is the 
epitome of regulatory flexibility.
    There is a rule in medicine, listen to the patient, they 
are telling you the answer. The second piece is, ignore the 
patients at your peril. What we have here is denying of the 
patient's story. It is the peril not of us, but of the patient 
because now the drugs are not being approved.
    I think you have hit the nail on the head here. If you are 
ignoring the patient, then why are you getting up in the 
morning and coming to do the work that you do with the FDA?
    Senator Gillibrand. Well said. Dr. O'Neill.
    Dr. O'Neill. Thank you. You know, obviously you have heard 
that patients are not outside of the drug development process. 
They are critical to it and advisory committees, as Annie had 
mentioned, are an important place where we can have that 
scientific dialog and hear from patients.
    Their experience is also science. It is human science. The 
interaction needs to come way before that, because by the time 
we get to an advisory board, tens of millions of dollars have 
been spent, maybe a decade has gone by. We have not treated 
potentially that many patients who needed treatment.
    Having a true collaborative dialog early in the process is 
essential and something--an opportunity that needs to be acted 
upon within the FDA. I think one other thing that we are 
understanding is key insights around risk tolerance. We also 
want safe medicines, but we also want the opportunity to save 
our children because those answers about a clinical trial come 
way down the road.
    As Mr. Campbell explained, real-world evidence, post-
marketing disease monitoring programs, this is where we need to 
be really focusing on these innovative ways. Maybe not so 
innovative, honestly, anymore, but more frequently used and 
supported ways to provide that longer term evidence to support 
accelerated approval.
    Senator Gillibrand. Mr. Campbell, did you want to add?
    Mr. Campbell. For sure. I think what we keep coming back 
to, and I think you hear the theme, is you have all the tools 
in place. You have the advisory committees. You have 
accelerated approval pathways.
    I think the frustration is when they are deployed 
inconsistently and without clarity from the sponsors and from 
the patient community and from the physicians in terms of how 
you end up, you know, meeting the expectation but then not 
coming to a positive resolution. There is one other piece that 
we haven't talked about, if I could just introduce that, which 
is the Rare Disease Innovation Hub. If we want to talk about 
things that Congress could proactively do.
    We have a tool that is modeled after what was very 
successful in oncology, the Center of Excellence, but my 
observation would be is it is underfunded and probably under 
empowered to do what it needs to do.
    When we think about advisory committees, when talk about 
staffing at the FDA, when we think consistency between 
reviewers, Congress could directly fund the Rare Disease 
Innovation Hub in a meaningful way that would allow us to train 
rare disease experts that could sit across review teams, across 
review divisions, and bring some of that consistency, that 
humanity, that humility, but that expertise that perhaps each 
of the individual teams or the new reviewer on the team doesn't 
quite have.
    Again, I think we have a lot of the tools that we need. We 
just need to encourage the FDA to use them in the right way and 
that is one example we haven't talked about here today where 
Congress could fund that directly and allow the FDA to make it 
a much more valuable tool for rare disease drug development.
    Senator Gillibrand. Thank you, Mr. Chairman.
    The Chairman. You know, when you hear the testimony, I 
think all of us internalize it. I have got six grandsons and a 
granddaughter and you know, thank God they don't--you know, 
everybody has got problems, right, but you know, they don't 
have a rare disease that is going to shorten their life.
    I can't imagine what a family is going through when they 
have a family member that has something and then they believe 
there is a possibility that something could change their life, 
and it doesn't happen. I mean, I would be pretty frustrated. I 
would be pretty--more than that. Ms. Kennedy, is it important 
for people to come to Congress and talk about their concerns 
with regard to the drug approval process?
    Ms. Kennedy. Well, I know you are asking me, but there are 
about 800 people on the Hill that would be happy to answer that 
question as well.
    Throughout this time here this morning, starting with your 
opening remarks, we have cited many laws that have been 
transformational for our rare disease community, and every 
single one of them started with a member of the community 
meeting with their elected official and talking about a 
roadblock that could be transformed and turn into a resource 
and a tool.
    Every single one of those laws has transformed lives and 
ultimately has saved lives. So the answer to your question is 
an emphatic yes, and we are so grateful for the time you take 
to be with our community, to listen to our community, to 
engage, and to become partners with all of us, so thank you.
    The Chairman. Does the FDA appreciate when you guys come 
here?
    Ms. Kennedy. I think many do, yes. Maybe some no, but I 
think overall, over the years, I have been in this space 30 
years and I think we have had strong partnerships with the 
agency and many times the agency has very much appreciated our 
support.
    The Chairman. Dr. Schmahmann, what--from a clinical 
standpoint, what happens to patients with progressive 
neurologic diseases when access to treatment is delayed due to 
the regulatory process rather than safety concerns?
    Dr. Schmahmann. They progressively deteriorate. They lose 
function. They can't live their lives, go to work, spend time 
with their family, make a living, be productive citizens of 
society in that way. They become part of the family that people 
have to take care of instead of taking care of the families 
themselves. Then they become progressively debilitated and then 
they die young.
    Then family members, in our case, see that. They see their 
future in the mirror. There is a high incidence of depression 
and, in fact, suicidality in this patient community as well. 
This is across the spectrum. This is not a motor control 
problem alone. This is a social, emotional, societal issue and 
the issue about medications that improve neurological function 
in real time work at the level of the physiology where brain 
cells are sick before they die.
    If you have a medication, even though it is not a gene 
therapy, you have medication like troriluzole, where we know 
the mechanism, and you stop the neurons from being so 
hyperactive that they die, you actually improve function and 
you slow disease over time, so you are modifying the disease.
    The absence of a medication that can treat the disease 
means that each day that this drug, troriluzole, and others 
like it are not being approved means patients are losing brain 
cells and are closer to death. It is heartbreaking to see, as 
you all said at the outset, and we are hoping that this can 
change from today.
    The Chairman. I think in your testimony you said that the 
FDA suggested withdrawing patients from compassionate use of 
care to evaluate whether their conditions would deteriorate 
despite physicians expressing the harm would be irreversible. 
So tell me about the--what are the ethical implications of 
that?
    Dr. Schmahmann. If you have a disease where there is a 
symptom like a migraine, for example, you can see if I stop the 
drug, will you get worse for a week or two, or a month, and I 
will put you back on drug, you are okay. In a neurodegenerative 
disease like these, and I am going to be--excuse me if I am 
provocative--the last time we had a catastrophe in medical 
science in the U.S. was between 1922 and 1972.
    I believe there was like a 40-year period, 1932 to 1972, 
when people with syphilis were not treated so that the doctors 
could see what happened to them, and the patients were not 
told. That is a case study for every person who is going into 
human studies research in the United States.
    We learn about that case. You cannot treat patients like 
guinea pigs. You have to have them on your story as part of the 
research collaborator, experts by experience. If we have a 
drug, as we do here, that is first safe and that bends the arc 
of the disease, and you want patients to come off that drug so 
you can see if they worsen, in other words if their brain cells 
are dying under your care, that is a poster child--it is 
Tuskegee version two, and it is entirely unacceptable. I reject 
it outright.
    They should not have recommended that and whoever did, I 
would suggest they take updated education sessions on clinical 
trials and on human studies research. It is not okay, Senator.
    The Chairman. I can't imagine doing that. Mr. Campbell, 
talk about inconsistent FDA standards, how it impacts 
timelines, costs, the ability of small biotech companies to 
survive. Is it easier to raise money if the FDA is 
inconsistent? Does that make your job easier?
    Mr. Campbell. No, is the candid answer, and you know, that 
is underlying all of this, right. We have created in the United 
States this rich ecosystem of innovation, which has been 
supported by Congress, supported by FDA over the years, 
supported by modern technology, and that brings in new 
companies that bring in new innovations and offer some of the 
therapies that we have talked about here today that are now 
stuck in front of this regulatory process.
    The reality is, and this is in my written testimony, the 
reality is for many small and mid-sized biotech companies, it 
takes decades to become profitable, which means we are going 
hand-in-mouth begging for dollars from investors. If there is a 
clear path forward and investors can be confident of an 
eventual return, then they will keep investing and the 
innovation ecosystem keeps going and going.
    If we continue to create this uncertainty, if we continue 
to create an uncertainty around manufacturing timelines, around 
approval timelines, around changing the goalposts again, I am 
confident that those investor dollars will go somewhere else.
    I will tell you transparently, having gone to the recent 
J.P. Morgan Healthcare Conference, which I am sure folks know 
is the big investor conference in our industry, I heard more 
opportunities about Chinese therapeutics and companies than 
ever before, and I don't think that is an accident.
    Ten, twenty years ago, we might have thought the science 
wasn't good. We might have distrusted the quality and the 
safety. I can tell you that the innovation there and the 
science is equally as good as ours.
    We still have an advantage, but if we are not careful, we 
are going to lose that advantage, and at the end of the day, 
the American patients suffer, the American economy suffers, and 
I am convinced that that is a real threat, in addition to the 
most important piece, which is making sure drugs get to 
patients faster.
    The Chairman. Dr. O'Neill, in progressive rare diseases, 
how should regulators account for the fact that clinical 
decline is often irreversible? Should the harm of waiting be 
weighed alongside uncertainty in the data? If so, how?
    Dr. O'Neill. Thank you. Yes, to call back to Dr. 
Schmahmann's points around this and about exposure to not being 
on drug, the risks of not treating this disease are known. You 
know, these are not in question.
    We know these children will be permanently, severely brain 
injured for the rest of their lives. There are critical, time-
sensitive neurodevelopmental windows in childhood when it is 
important to intervene to be able to receive the maximum 
benefit. There is a continuum of this, but earlier is always 
better.
    What we are still hearing as recommended to sponsors is 
that observational, or no treatment, or placebo controlled 
trials are being recommended for these pediatric conditions. 
This is very, very troubling when we know that they will become 
brain injured. We have also seen--you know, when parents ask me 
about this, I have to kind of step back and think, oh my 
goodness, I know what a perfect science experiment looks like.
    Yes, that is the perfect science experience, but these are 
children. You cannot do good medicine unless you are putting 
the patients first and following the ethics of medicine and we 
have heard changes around the use of animals in preclinical 
studies. Just last April, the FDA published its roadmap to 
reducing animal testing in pre-clinic studies, and this says, I 
quote, "due to the limitations of animal testing as well as 
ethical concerns about animal testing, there have been 
increased focus within the scientific community on new approach 
methodologies."
    We are concerned about the ethics of animal testing more 
than we are concerned about the ethics of allowing children to 
be brain injured in clinical trials, and I think we all need a 
gut check on that.
    The Chairman. Would any of you like to talk about what 
patients and caregivers tell you about their willingness to 
accept uncertainty or incomplete data when the alternative is 
no treatment at all?
    Dr. Schmahmann. I think it starts off with safety. Nobody 
likes side effects, and patients do want to know that the 
medications are safe, or the approaches are safe. Given that 
piece, if we can make a comment about safety, the degree to 
which the medication works or not is often something that 
patients, I think, are willing to take on.
    We can certainly hear from the others about that and the 
other rare diseases. In our space, knowing that the medications 
we have available are safe, and have been shown in other 
circumstances, patients are not just willing, they are--we are 
getting emails every day from people around the world, what 
trials do you have for me that I can use to try and slow down 
the process of my disease?
    Ms. Kennedy. Yes. I really appreciate that question, and I 
think my response would be that for each subpopulation within 
each condition, within each targeted therapy, that 
consideration would be very different, which is why Congress 
authorized the use of the benefit-risk framework within the 
consideration of regulatory review. That is one of the things 
that we are concerned about is not being applied.
    We don't know how it is being used. One of the things that 
we are asking for today is more questioning around how are 
these tools being utilized, because every community for every 
clinical trial within every subpopulation of that community 
will approach that threshold for risk tolerance differently.
    That is a super important question, Senator, and we are 
just not sure that that is being questioned the way it was 
intended for the tailorization that is required for rare 
disease therapeutic development.
    The Chairman. Mr. Campbell, can I ask you a separate 
question? How important is transparency from the FDA in 
maintaining trust with rare disease communities? What happens 
when explanations for delay are unclear or incomplete?
    Mr. Campbell. You know, I feel like as sponsors, 
manufacturers, we have a great duty to our patients. I think 
somebody--one of the Senators asked me why I am in this 
business. I will tell you, you know, it is for the patients, 
but when you have a chance to develop a therapy for people 
living with a rare disease, it sort of gets in your blood. You 
also, then you bear a great responsibility.
    I feel, I think, like sponsors are at the front lines, in 
front of the agency trying our best to get those drugs over the 
finish line. If we fail to do that for any reason, we owe it to 
the patients, to the community, to the caregivers to give them 
an explanation. When there is no good explanation or when the 
explanation is a crack on the floor, you know, that is just not 
good enough.
    I think I really do believe that sponsors bear some of that 
responsibility. I think it works best when we truly work 
together. Congress has the tools. The FDA has proven itself 
over time to be very effective in working with sponsors. I 
shared our story, which was an incredible, innovative 
regulatory science, medical science that helped thousands of 
patients.
    If you don't have that transparency, and if you do not have 
that consistency then, you know, we all lose, and I really 
believe that we are at the center of that. It pains me, you 
know, to hear these stories.
    We are not in that position today as Amicus, but we owe a 
responsibility to these people who are giving their lives to 
participate in clinical studies who have so much hope, we owe 
them clarity and we all do. Everybody who is involved in that, 
including the regulators.
    The Chairman. Ranking Member Gillibrand, you want to say 
anything before we close?
    Senator Gillibrand. I would like the audience members who 
have pictures of their loved ones to stand please so we can see 
their loved one. Thank you for coming to represent them. Thank 
you all. I want to just thank our guest who is in the corner 
who has been so well behaved this entire time. I am very proud 
of her for being such a good girl. Just thank you all for being 
here today. This has been an extremely powerful hearing. We 
have gotten some amazing testimony, and I am very hopeful that 
we will find better solutions so that we can all work together 
to get these cures that our loved ones so desperately need. 
Thank you all.
    The Chairman. I want to thank everybody for being here. I 
want to thank the Ranking Member for this. We have been doing 
this for a little over a year, and we have been able to do a 
lot of things together.
    What we heard today was not abstract policy theory. We 
heard from Mr. Campbell that 95 percent of rare diseases still 
have no approved treatment. At the current pace, it could take 
more than a century to meaningful close that gap. We heard Dr. 
Schmahmann about a multi-year data set supported by real-world 
evidence and natural history comparisons, showing meaningful 
showing of disease progression, yet still unable to clear the 
regulatory bar.
    We heard from Ms. Kennedy that at least 23 rare disease 
therapies received complete response letters in the past year, 
even as advisory committee meetings declined, raising concern 
about whether the flexibility Congress authorized is being 
applied consistently. We are reminded that for some patients, 
success is not an abstract endpoint, but the ability holds one 
breath long enough to survive another moment.
    I recently spoke with Commissioner Makary. It was clear 
that the FDA's framework was built for common diseases, not 
rare to ones. He is implementing reforms like the plausible 
mechanism pathway, greater flexibility for gene therapies, and 
strengthening the rare disease innovation hub. We look forward 
to working with him to ensure those changes are applied 
consistently and urgently for patients. He inherited a broken 
system, and the FDA cannot be fixed overnight.
    That said, he has made significant progress, and I am 
completely encouraged by the reforms President Trump has 
empowered Commissioner Makary to make at the FDA, and I know he 
cares deeply about getting results and making sure the United 
States remains the world's leader for innovation and treatment 
of rare diseases.
    Taking together the testimony presented before our 
Committee today makes one thing clear, the question is not 
whether to protect safety, it is whether the system is moving 
with the urgency Congress intended and patients require. The 
Committee will continue exercising oversight to ensure that 
flexibility enacted into law becomes reality in practice.
    I look forward to continuing work with our members. If any 
Senator has additional questions for the witnesses or 
statements to be added, the hearing record will be open until 
next Wednesday at 5:00 p.m. Thanks everybody for being here.
    [Whereupon, at 11:05 a.m., the hearing was adjourned.]
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                                APPENDIX
      
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                      Prepared Witness Statements

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                        Questions for the Record

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                 U.S. Senate Special Committee on Aging

 "From Regulator to Roadblock: How FDA Bureaucracy Stifles Innovation"

                           February 26, 2026

                        Questions for the Record

                             Annie Kennedy

                        Senator Raphael Warnock

    Question:

    Over the past few decades, the FDA has adopted strategies 
to accelerate the development of treatments for ultra-rare 
diseases. These strategies have included the Support for 
Clinical Trials Advancing Rare Disease Therapeutics Pilot 
Program, Rare Disease Evidence Principles, and the Plausible 
Mechanism of Action Framework. However, there are many rare 
diseases that still need treatments.
    What would be the advantages of the FDA extending the above 
strategies to other rare diseases? How can Congress ensure the 
FDA balances acceleration and thoroughness in its review of 
potential rare disease treatments?

    Response:

    We have been following closely the recent agency 
announcements, including the Rare Disease Evidence Principals 
(RDEP) initiative, the Plausible Mechanism Framework, the 
establishment of the Rare Disease Innovation Hub in 2024, and 
the implementation of new guidance documents and regulatory 
science pilot initiatives contained in PDUFA VII (10/1/2022 - 
9/30/2027).
    The application of these programs and policies can shape 
the prospects of rare disease therapy development for a given 
community, drive investment into one area and out of another, 
and determine how patient advocacy organizations allocate 
precious resources. For a variety of reasons the ways in which 
available guidances, programs, and pathways can be applied to 
different subpopulations of rare diseases differ. Multiple 
factors have led to some rare disease communities having 
greater success in leveraging FDA's regulatory flexibility 
including population size, therapeutic modality, disease 
characterization, extent of diagnostic delays, age of onset, 
and others.
    We are encouraged by the intent signaled by FDA's most 
recent initiatives, RDEP and the Plausible Mechanism Framework, 
however, more information is needed to understand how the 
Agency plans to operationalize these new approaches for 
products in today's pipeline and beyond, and which 
subpopulations of rare diseases stand to benefit initially, and 
over the longer term.
    We encourage additional dialogue and input from the 
community into these new initiatives as even the best ideas 
need the benefit of robust dialogue and operational details for 
them to have the intended effect.
    Specific to the RDEP announcement - this announcement 
appears to be responsive to calls for more predictability in 
the regulatory process, but more details will be needed before 
we have a detailed reaction. Many rare disease communities may 
not realize the program's benefits due to its narrow focus; 
however, it can provide valuable insights for expansion if 
appropriate metrics and evaluation methods are incorporated 
from the outset.
    We are eager to hear more details on how RDEP will be 
operationalized, as well as a better understanding of how 
RDEP's requirements for pre-specifying the trial requirements 
will be handled, given the nature of many rare disease trial 
designs.
    Regarding the Plausible Mechanism Framework, we are 
encouraged by the release of the draft Guidance, and what it 
represents for the eligible communities for whom traditional 
approaches to clinical trials and regulatory requirements are 
fundamentally at odds with the reality of their conditions. We 
are grateful to the FDA for taking on this challenge of 
ensuring no disease is too rare to deserve treatment. And we 
are incredible grateful to the many families and experts who 
applied their personal expertise to yield transformational 
change.
    We also recognize that for many in our rare disease 
community, the Plausible Mechanism Framework will not apply, 
and we urge FDA leadership to continue pursuing solutions that 
will ensure the tools and policies that Congress has created 
over decades, are deployed in a predictable and consistent 
manner that can unleash scientific innovation and speed safe 
and effective therapies to patients across the more than 10,000 
rare diseases. The EveryLife Foundation team is in the process 
of closely reviewing the recently released draft Guidance.
    Regarding the Rare Disease Innovation Hub and opportunities 
yielding from PDUFA VII Pilot Programs, we are hopeful that the 
opportunities stemming from these PDUFA VII investments will be 
applied more broadly across rare disease product development. 
The Rare Disease Innovation Hub is well positioned to be a 
catalyst of progress by spearheading the dissemination of data, 
case studies, and other learnings resulting from these pilots 
and experiences with the application of regulatory flexibility 
tools more broadly.
    Since 1983, Congress has created incentives and policies 
that recognize the inherent complexities in developing 
treatments for rare diseases. Congress has explicitly given the 
FDA authority to uphold the highest standards of regulatory 
safety and rigor, while applying tailored approaches (i.e. 
"regulatory flexibility"). Such approaches include:

      Establishment of the accelerated approval pathway
      Consideration of the totality of evidence in the 
regulatory review
      Inclusion of Patient Experience Data (PED) in clinical 
trial design & regulatory processes
      Utilization of innovative clinical trial designs and 
real-world evidence (RWE)

    Nearly 1,400 orphan-designated therapies are changing the 
lives of patients and families, but 95% of rare diseases remain 
without an FDA-approved treatment.
    Congress must continually ensure that FDA review statutes 
keep pace with the science and are designed to work across the 
spectrum of rare diseases, from n-1 to just under 200,000, and 
from pediatric to adult populations. Congress should look to 
address gaps more regularly, ideally more often than the 
typical practice of moving regulatory legislation alongside the 
five-year PDUFA reauthorization window allows. Congress should 
regularly engage in dialogue with the Agency leadership and 
rare disease stakeholders, seek comprehensive metrics to 
understand how the Agency is applying regulatory flexibility, 
and ensure the Agency has adequate resources, such as funding 
for the Rare Disease Innovation Hub, to optimize their ability 
to apply tailored approaches to rare disease product 
evaluation.

    Question:

    As part of his sweeping reductions-in-force (RIFs) of 
Department of Health and Human Services (HHS) employees, HHS 
Secretary Robert F. Kennedy dismissed 3,500 Federal Drug 
Administration (FDA) employees in April 2025. The RIFs targeted 
employees across the agency, including advisory committee 
staff.
    You mentioned that the FDA held far fewer advisory 
committee meetings in 2025 relative to 2024 and that this 
drastic drop meant fewer opportunities for experts and patients 
to share information to inform the FDA's decision-making. What 
are the ramifications of last year's RIFs at the FDA for the 
development and treatment of illnesses that do not yet have a 
cure?

    Response:

    Significant leaders the rare disease community has built 
relationships with over the years have either resigned or been 
laid off in the last 12 months, resulting in the loss of 
powerful allies and institutional knowledge that have generated 
the progress the rare disease community has seen over the last 
decade. However, thousands of committed public servants remain, 
and the EveryLife Foundation, together with our community, is 
committed to policies that will support and enhance the 
Agency's rare disease capacity and expertise.
    Rare disease product reviews occur in every division and 
product Center at the FDA. With the appropriate resources, the 
Rare Disease Innovation Hub is poised to enhance its role as 
the FDA's coordinating office to optimize rare disease 
expertise, processes, and engagement with stakeholders across 
all therapeutic areas, including drugs, cell and gene 
therapies, and medical devices. Given the departure of 
experienced staff, the importance of a robust Rare Disease 
Innovation Hub is magnified. The Hub's first full year of 
operations has laid the foundation for meeting this moment of 
opportunity if institutional support and resources are 
enhanced.

    Question:

    How can Congress conduct oversight over the FDA to ensure 
the agency continues to hold advisory committee meetings and 
review rare disease treatments?

    Response:

    We are concerned about the dramatic decline in 
opportunities to leverage external scientific, clinical, and 
patient-community insights to inform deliberations on complex 
rare-disease product reviews. While not every product 
application requires an advisory committee, where relevant, 
their use was one of the few ways the Agency discussed its 
approach to the review in public and heard from clinicians who 
treat patients and run trials, and from the patients and 
families who took part. This additional insight affords review 
teams with another data point to consider among the totality of 
evidence they must balance when determining how to apply the 
regulatory flexibility tools that Congress has authorized.

    As I encouraged Congress in my testimony, Congress should 
conduct outreach to the Agency to understand its approach to 
the following:

      The application of the accelerated approval pathway to 
rare disease therapies;
      Improving the predictability and consistency of the 
application of regulatory flexibility; and
      Resuming the use of Advisory Committee Meetings to 
receive external expertise on product reviews and key policy 
topics.

    Based on this engagement and the Agency's responses, we 
encourage Congress to identify opportunities for additional 
public dialogue with the Agency and rare disease stakeholders 
to identify a path forward that will ensure sustainable, 
transparent, and predictable processes for leveraging external 
expertise in relevant product reviews and to inform overall 
rare disease regulatory science approaches moving forward.

                 U.S. Senate Special Committee on Aging

 "From Regulator to Roadblock: How FDA Bureaucracy Stifles Innovation"

                           February 26, 2026

                        Questions for the Record

                            Bradley Campbell

                        Senator Raphael Warnock

    Question:

    Approximately one in ten Georgians live with a rare 
disease. Many of these individuals, including older adults, do 
not have access to life-saving treatments due to incomplete 
scientific knowledge of their disease and limited funding. 
Families seeking treatments that were reviewed under a priority 
voucher program are also experiencing delays due to the 
prolonged FDA approval process.
    How can Congress reduce regulatory barriers to expedite the 
FDA's approval process for rare disease treatments while 
maintaining the safety and quality of these treatments?

    Response:

    Senator Warnock, thank you for this thoughtful question. As 
noted in my testimony, I believe there are low-hanging fruit 
that we can seize while still maintaining FDA's "gold standard" 
for safety and efficacy:

      Speeding up approval of early phase clinical trials
      Harnessing innovative endpoints based on biomarkers
      Expanding the use of real-world evidence
      Streamlining manufacturing inspections

    In cases where there is residual uncertainty about the 
durability or extent of patient benefit for promising 
therapies, real-world data should be collected post-approval 
via the Accelerated Approval pathway.\1\ If that data does not 
bear out patient benefit, the agency should consider 
withdrawing that treatment in consultation with the patient 
community. When it comes to rare diseases, patients and their 
families are the true experts, and their voices need to be 
respected as such.
---------------------------------------------------------------------------
    \1\ Examples of rare-disease therapies that entered the market via 
FDA Accelerated Approval and later converted to full approval include 
sparsentan for primary IgA nephropathy, agalsidase beta for Fabry 
disease, and delandistrogene moxeparvovec-rokl for Duchenne muscular 
dystrophy.
---------------------------------------------------------------------------
    FDA already has Congressionally granted authority to do 
everything I listed above. The challenge is simply doing them 
consistently. This is where Congressional oversight is vital.

    Question:

    How do bipartisan initiatives like the FDA Pediatric 
Priority Review Voucher program, which I was glad to see 
reauthorized recently, help incentivize innovation for rare 
disease treatments?

    Response:

    Senator Warnock, we are deeply grateful to Congress for 
reauthorizing the FDA's Pediatric Priority Review Voucher (PRV) 
program.
    Small and mid-size biotech companies are the driving force 
behind U.S. drug development for all diseases, but particularly 
for rare diseases. These companies are often pre-commercial, 
meaning they are years-to-decades from sustainable 
profitability.
    When a company with a PRV voucher receives FDA approval, 
the sponsor can sell that voucher, sometimes for hundreds of 
millions of dollars. That funding is a critical lifeline for 
continued operations when the alternative is bankruptcy.
    Rare pediatric diseases that have benefited from PRVs 
include pediatric neuroblastoma, the most common cancer in 
infants; spinal muscular atrophy (SMA), the most common genetic 
cause of infant mortality; and epidermolysis bullosa, which 
causes fragile, blistering skin.
    There we no treatments for any of these diseases before 
Congress created the PRV program in 2012.
    The PRV program has no cost to taxpayers, but when 
investors are considering whether to fund an early-stage rare 
disease company, having a PRV designation can be decisive.
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                       Statements for the Record

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